Risk Calculators

Aortic Root Z-score Calculator for Children

• Parameterz: http://www.parameterz.com/sites/aortic-root
• CCPCRN Z-Score: https://www.rchsd.org/zscore/?modality=echo&study=dallaire2025
• Pediatric Heart Network Z-Score: http://www.parameterz.com/refs/lopez-circimaging-2017
• Boston Z-Score Calculator: https://marfan.org/dx/zscore-children/

Aortic Root Z-score Calculator for Adults

• Parameterz: http://www.parameterz.com/sites/aortic-root
• Boston Z-Score Calculator: https://marfan.org/dx/z-score-adults/

Aortic Size Index

• Maximum aortic size divided by surface area (https://www.annalsthoracicsurgery.org/article/S0003-4975(05)01031-3/fulltext#secd17620610e1700)

Clinical Scoring System for Early Onset (Neonatal) Marfan syndrome

• Zarate et al.: https://www.gimjournal.org/article/S1098-3600(22)00706-7/fulltext

Aortic Dimensions in Turner syndrome

• Quezada et al.: https://onlinelibrary.wiley.com/doi/abs/10.1002/ajmg.a.37208
• Parameterz: http://www.parameterz.com/refs/quezada-ajmg-2015

Cardiovascular Outcomes in Aortopathy: GenTAC Registry of Genetically Triggered Aortic Aneurysms and Related Conditions

• Holmes et al.: https://www.jacc.org/doi/full/10.1016/j.jacc.2022.03.367

Aortic Cross-Sectional Area/Height Ratio

• Masri et al.: https://www.ahajournals.org/doi/10.1161/circulationaha.116.022995

Comparative Risks of Initial Aortic Events Associated With Genetic Thoracic Aortic Disease

• Regalado et al.: https://www.jacc.org/doi/10.1016/j.jacc.2022.05.054

Vertebral Tortuosity Index

• Morris et al.: https://www.ahajournals.org/doi/full/10.1161/CIRCULATIONAHA.110.990549#d3e376